Familial clustering of Leiomyomatosis peritonealis disseminata: an unknown genetic syndrome?
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چکیده
منابع مشابه
Familial clustering of Leiomyomatosis peritonealis disseminata: an unknown genetic syndrome?
BACKGROUND Leiomyomatosis peritonealis disseminata (LPD) is defined as the occurrence of multiple tumorous intraabdominal lesions, which are myomatous nodules. LPD is a rare disease with only about 100 cases reported. The usual course of LPD is benign with the majority of the patients being premenopausal females. Only two cases involving men have been reported, no syndrome or familial occurrenc...
متن کاملLeiomyomatosis peritonealis disseminata: a case report.
Leiomyomatosis peritonealis disseminata (LPD) is a very rare disease characterized by formation of multiple smooth muscle tumor or nodules disseminated throughout the omental and peritoneal surfaces. It is a benign disease of unknown etiology which usually occur in women of reproductive age. The tumor may originate from the mesentery, the omentum and even the peritoneum covering the abdominal w...
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BACKGROUND Leiomyomatosis peritonealis disseminata (LPD) is a rare condition that occurs in reproductive-age women. The pathogenesis of LPD is considered to be related to female sex hormones. CASE REPORT A 30-year-old woman who had undergone an ovariectomy due to calcified thecoma at 24 years of age and had delivered a baby boy at 29 years of age showed abnormal abdominal-pelvic masses in a c...
متن کاملLeiomyomatosis peritonealis disseminata presenting as omental torsion.
Leiomyomatosis peritonealis disseminata is usually asymptomatic or mimics widespread malignancy; acute presentation is rare. We describe a patient with right iliac fossa and lower abdominal pain. Two masses were detected via computed tomography, but at surgery, one of these implanted leiomyomas had undergone acute omental torsion. This case illustrates a rare complication of omental leiomyoma t...
متن کاملLeiomyomatosis peritonealis disseminata: case report and review of the literature.
Leiomyomatosis peritonealis disseminata (LPD) is typically a benign and rare disorder found in female patients, prior to menopause. It can be found in the subperitoneal or peritoneal spaces and is represented by multiple different sized myomatous nodules (smooth muscle tumors). Additionally, it has also been found in women after menopause as well as in men. Despite the fact that high levels of ...
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ژورنال
عنوان ژورنال: BMC Gastroenterology
سال: 2005
ISSN: 1471-230X
DOI: 10.1186/1471-230x-5-33